Durable hypogammaglobulinemia associated with thymoma (Good syndrome).

نویسندگان

  • Atsushi Kitamura
  • Yuichi Takiguchi
  • Naobumi Tochigi
  • Shun-ichi Watanabe
  • Seiichirou Sakao
  • Katsushi Kurosu
  • Nobuhiro Tanabe
  • Koichiro Tatsumi
چکیده

Good syndrome, characterized by hypogammaglobulinemia and acquired immunodeficiency, is a rare condition associated with thymoma. A 67-year-old woman, who 4 months previously had a thymoma resected, presented with generalized hypogammaglobulinemia with a severely decreased B cell population as demonstrated by flow cytometry. She was diagnosed as having bacterial mediastinitis associated with Good syndrome. For the subsequent 6 years, she suffered from repeated serious bacterial infections. As this paraneoplastic syndrome is not resolved by tumor removal, careful management with intensive infection-control using antibiotics and intravenous immunoglobulins is required for the long term. Serum immunoglobulin levels should be evaluated for patients with thymoma and suspected vulnerability to infection.

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عنوان ژورنال:
  • Internal medicine

دوره 48 19  شماره 

صفحات  -

تاریخ انتشار 2009